Search on: SARCOSINE DEHYDROGENASE 
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Descriptor English:   Sarcosine Dehydrogenase 
Descriptor Spanish:   Sarcosina-Deshidrogenasa 
Descriptor Portuguese:   Sarcosina Desidrogenase 
Synonyms English:   Dehydrogenase, Monomethylglycine
Dehydrogenase, Sarcosine
Monomethylglycine Dehydrogenase
N-Demethylase, Sarcosine
Sarcosine N Demethylase
Sarcosine N-Demethylase  
Tree Number:   D08.811.682.662.582.550
Definition English:   A LIVER mitochondrial matrix flavoenzyme that catalyzes the oxidation of SARCOSINE to GLYCINE and FORMALDEHYDE. Mutation in the enzyme causes sarcosinemia, a rare autosomal metabolic defect characterized by elevated levels of SARCOSINE in BLOOD and URINE. 
History Note English:   2006(1976); use OXIDOREDUCTASES, N-DEMETHYLATING, & SARCOSINE 1976-1979 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   50631 
Unique Identifier:   D050892 

Occurrence in VHL:
 

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